Abstract

Objective: The aim of this study was to determine the effect of maternal feeding behavior on nutrition status and behaviors of children with phenylketonuria (PKU).


Material and Methods: The PKU Family Association’s 2-11 year-old children and their mothers were administered face to face questionnaire to determine the sociodemographic characteristics of the family, mothers’ feeding attitudes of their children and anthropometric measurements of the children. One-day food consumption records were taken retrospectively, daily energy, macro and micro nutrients were calculated by the Nutrition Information System computer program and the level of meeting daily requirements was determined. Children’s anthropometric evaluation was done with WHO AnthroPlus Program, weight for age z-score (WAZ), height for age z-score (HAZ) and BMI for age z-score (BAZ) were calculated.

Results: It was found that the mean WAZ value of the children was 0.1 ± 0.9, the HAZ value was -0.3 ± 1.7 and the BAZ value was 0.4 ± 1.8 and the feeding behavior of the mother affected the anthropometric measures of the child (p<0.05). While energy requirements were met by 77.7%, protein, vitamin B6, B12 and C intake was above the recommendations and folate intake was below the recommendations. It was detected that the feeding behavior of the mother when child refused food intake, did not affect the child’s blood phenylalanine level and macro-micro nutrient intake (p>0.05). The majority of the children (86.7%) were found to be compatible with their diet and their mothers were found to higher age (p = 0.03). It was determined that the majority of mothers (80.0%) did not give up when they refused to feed and that feeding (26.7%) after feeding them for a while and trying to feed them into games (23.3%).


Conclusion: Feeding attitudes of mothers affect the nutritional status of children. In order to increase compliance with the lifelong dietary treatment of children with PKU, supportive nutrition education for parents should be planned and provided part of the treatment.

Keywords: Phenylketonuria,, Metabolic disorders, Eating behavior,, Nutritional status,

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How to cite

1.
Aktaç Ş, Öğren G, Fereli S, Karğın D, İçen H. The Effect of Maternal Feeding Behaviours on Eating Attitudes and Behaviours of Children with Phenylketonuria. Turk J Pediatr Dis [Internet]. 2021 May 25 [cited 2025 May 24];15(3):174-80. Available from: https://turkjpediatrdis.org/article/view/783