Öz
Biliary atresia is a rare and fatal cholestatic disorder characterized by progressive obliteration of the extrahepatic and intrahepatic bile ducts, typically presenting during the neonatal period. Ethology remains uncertain, although immune-mediated injury, viral triggers, and developmental anomalies have been implicated.
Kasai portoenterostomy is the primary treatment for biliary atresia, with optimal outcomes achieved when performed within the first 60 days of life. Despite early intervention, many patients experience progressive cirrhosis and portal hypertension. Liver transplantation remains the definitive therapeutic option.
The timing of liver transplantation in early infancy remains controversial. A primary concern is increased mortality associated with the inability to administer live childhood vaccines to infants transplanted before six months of age, thereby elevating the risk of subsequent life-threatening infections.
A 6-kg infant was diagnosed with biliary atresia and underwent surgery 84 days of age. Robotic-assisted Kasai portoenterostomy was performed to maintain bile flow until transplantation and to minimize adhesion formation, both of which are beneficial for subsequent transplantation. This report presents the technical aspects of the procedure.
Kaynakça
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