Abstract

Kawasaki disease (mucocutaneous lymph node syndrome) is a systemic vasculitic syndrome with unknown etiology which occurs predominantly in children younger than 5 years.It is the second common cause of vasculitis following Henoch-Schonlein vasculitis in childhood. The most important complication of the disease is coronary artery aneurysm. For that reason, early diagnosis and therapy is very important for good prognosis. Kawasaki disease has no certain diagnostic criteria. Because of atypical or incomplete cases, Kawasaki disease should be considered in any infant or young child with prolonged and unexplained fever and these patients should be evaluated by echocardiography for cardiac complications. We present a 5.5 month old boy referred to our hospital for prolonged fever, developing coronary artery aneurysm and diagnosed as Kawasaki disease to emphasize the importance of early diagnosis and therapy once more

Keywords: Kawasaki disease, infant, coronary artery aneurysm

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How to cite

1.
Özaydın E, Ece İ, Gökdağ B, Alpan N, Köse G. KAWASAKI DISEASE. Turk J Pediatr Dis [Internet]. 2010 Dec. 1 [cited 2025 Jul. 12];4(1):36-41. Available from: https://turkjpediatrdis.org/article/view/92