Sacrococcygeal teratomas originate from the embryonic germ cell layers and are the most common neonatal tumor. The tumor is usually benign and has solid and cystic structures, but may be prone to bleeding due to increased vascularization. The anesthesia management of these cases is challenging due to the risk of bleeding, hemodynamic instability, electrolyte imbalance, hypothermia, and acidosis. Complications may cause serious perioperative morbidity and mortality. In this case report, important steps in the anesthesia management of a female patient, who was born at 29 weeks and 6 days of gestation, weighed 2190 g, and was operated for a mass compatible with sacrococcygeal teratoma on the 3rd day of her life were emphasized. The importance of preoperative preparation, invasive arterial monitoring, close follow-up of blood, fluid and electrolyte replacement is presented in the light of the literature.

Keywords: Anesthesia Management, Giant Sacrococcygeal Teratoma, Premature Newborn