Abstract

Idiopathic pulmonary hemosiderosis (IPH) is a rare disorder of unknown etiology and characterized with iron deficiency anemia (IDA), recurrent attacks of alveolar hemorrhage and hemoptysis. The vast majority of cases occur during childhood. Clinically, it is presented with symptoms such as hemoptysis, respiratory distress during attacks of alveolar hemorrhage, parenchymal infiltrates on chest x-ray and secondary iron deficiency anemia. Therefore, differential diagnosis should be done to rule out other diseases causing recurrent respiratory distress and iron deficiency anemia. We present a 2-year-old patient with a history of recurrent lower respiratory tract infection and cystic fibrosis who was diagnosed with IPH. The diagnosis of the case was confirmed by seeing hemosiderin-laden macrophages in bronchoalveolar lavage fluid. Remission was achieved with steroid treatment. 

Keywords: Iron deficiency anemia, Cystic fibrosis, Pulmonary hemosiderosis

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How to cite

1.
Büyükavcı M, Erkun O, Orhan MF. A Rare Entity in the Differential Diagnosis of Recurrent Pulmonary Infection and Refractory Iron Deficiency Anemia: Idiopathic Pulmonary Hemosiderosis. Turk J Pediatr Dis [Internet]. 2020 Nov. 30 [cited 2025 May 24];14(6):531-5. Available from: https://turkjpediatrdis.org/article/view/653