Abstract







 Gorham-Stout disease is a complex disease in which lytic lesions of bone tissue are accompanied by chylothorax and abdominal lymphangioma. The etiology is still unknown. The diagnosis is made by the patient’s clinical and laboratory findings and biopsy results. It may be fatal depending on the organs involved. Although many treatments have been described, successful results have been reported with interferon alpha 2b in recent years. We discuss the clinical diagnosis and treatment of a 5-year-old female patient with osteolytic lesions in the bones after she was referred with chylothorax 

Keywords: Child, Gorham-Stout Syndrome, Interferon Alfa-2b

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Copyright and license

How to cite

1.
Aydın E. A Rare Cause of Chylothorax in Children: Gorham-Stout Syndrome. Turk J Pediatr Dis [Internet]. 2019 Mar. 21 [cited 2025 May 25];13(1):36-9. Available from: https://turkjpediatrdis.org/article/view/638