Öz


 Gorham-stout hastalığı kemik dokusunun litik lezyonları ile birlikte şilotoraks ve abdominal lenfangiomanın olabildiği kompleks bir hastalıktır. Etiyolojisi halen bilinmemektedir. Tanısı hastanın kliniği, laboratuvar bulguları ve biyopsi ile konulur. Tutulan organlara göre ölümcül seyredebilir. Birçok tedavi tariflenmiş olmakla birlikte son yıllarda interferon alfa 2b ile başarılı sonuçlar bildirilmiştir. Biz burada şilotoraks ile başvuran, kemikte litik lezyonları olan 5 yaşındaki kız hastanın klinik tanısı ve tedavisini tartıştık. 

Anahtar Kelimeler: Çocuk, Gorham-Stout Sendromu, Interferon Alfa-2b

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Telif hakkı ve lisans

Nasıl atıf yapılır

1.
Aydın E. Çocuklarda Nadir Bir Şilotoraks Nedeni: Gorham-Stout Sendromu. Turk J Pediatr Dis [Internet]. 2019 Mar. 21 [cited 2025 May 25];13(1):36-9. Available from: https://turkjpediatrdis.org/article/view/638