Abstract

Polymicrogria is a relatively common malformation of cortical development. The perisylvian region is the most common location of the polymicrogria. Bilateral perisylvian polymicrogria is a syndrome characterized by epilepsy, pseudobulbar palsy and cognitive impairment. Arthrogryposis has been reported in the minority of the cases. Here, a case with bilateral perisylvian polymicrogria syndrome associated with congenital arthrogryposis is presented to draw attention to this unity

Keywords: Arthrogryposis, Epilepsy, Polymicrogyria

References

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Copyright and license

How to cite

1.
Gürkaş E, Kurt ANÇ, Hirfanoğlu T, Serdaroğlu A, Oğuz KK. Congenital Bilateral Perisylvian Polymicrogyri Syndrome with Congenital Arthrogryposis. Turk J Pediatr Dis [Internet]. 2013 Apr. 1 [cited 2025 May 23];7(1):37-9. Available from: https://turkjpediatrdis.org/article/view/248