Öz
Abernethy malformasyonu birçok farklı klinik bulgu ile görülebilen çok nadir bir splanknik venöz sistem anomalisidir. Bu olgu sunumunda klinik bulgusu olmadan tetkikler sonucunda rastlantısal olarak Abernethy malformasyonu saptanan ve karaciğerde kitleleri bulunan 5 aylık kız olgu sunulmaktadır. Malformasyonun klinik bulguları ve olası komplikasyonların önemi vurgulanmaktadır.
Anahtar Kelimeler: Çocuk, Portal ven, Vasküler malformasyon
Referanslar
- Abernethy J, Banks J. Account of two instances of the uncommon formation in the viscera of the human body. Philos Trans 1793; 83:59-66.
- Mistinova J, Valacsai F, Varga I. Congenital absence of the portal vein: Case report and a review of literature. Clin Anat 2010; 23: 750-8.
- Morgan G, Superina R. Congenital absence of the portal vein: two cases and a proposed classifi cation system for portasystemic vascular anomalies. J Pediatr Surg 1994; 29: 1239-41.
- Gocmen R, Akhan O, Talim B. Congenital absence of the portal vein associated with congenital hepatic fi brosis. Pediatr Radiol 2007; 37: 920-4.
- Gallego C, Velasco M, Marcuello P, Tejedor D, De Campo L, Friera A. Congenital and acquired anomalies of the portal venous system. Radiographics 2002;22:141-59.
- Ratnasamy C, Kurbegov A, Swaminathan S. Cardiac anomalies in the setting of the Abernethy malformation of the portal vein. Cardiol Young 2007;17:212-4.
- Hu GH, Shen LG, Yang J, Mei JH, Zhu YF. Insight into congenital absence of the portal vein: Is it rare?. World J Gastroenterol 2008;14:5969-79
- Kim MJ, Ko JS, Seo JK, Yang HR, Chang JY, Kim GB, et al. Clinical features of congenital portosystemic shunt in children. Eur J Pediatr 2012;171:395-400.
- Witters P, Maleux G, George C, Delcroix M, Hoffman I, Gewillig M, et al. Congenital veno-venous malformations of the liver: Widely variable clinical presentations. J Gastroenterol Hepatol 2008;23:390-4.
- Franchi-Abella S, Branchereau S, Lambert V, Fabre M, Steimberg C, Losay J, et al. Complications of congenital portosystemic shunts in children: Therapeutic options and outcomes. J Pediatr Gastroenterol Nutr 2010;51:322–30.
- Singhal A, Srivastava A, Goyal N, Vij V, Wadhawan M, Bera M, et al. Successful living donor liver transplant in a child with Abernethy malformation with biliary atresia, ventricular septal defect and intrapulmonary shunting. Pediatr Transplant 2009; 13: 1041–7.
- Passalacqua M, Lie KT, Yarmohammadi H. Congenital extrahepa- tic portosystemic shunt (Abernethy malformation) treated endovas- cularly with vascular plug shunt closure. Pediatr Surg Int 2012; 28:79-83.
Telif hakkı ve lisans
Nasıl atıf yapılır
1.
Appak YÇ, Tarhan S, Doğan G, Kasırga E. Abernethy Malformasyonu: Konjenital Ekstrahepatik Portokaval Şantın Nadir Nedeni. Turk J Pediatr Dis [Internet]. 2016 Apr. 1 [cited 2025 May 24];10(1):53-6. Available from: https://turkjpediatrdis.org/article/view/418