Öz

Bartter sendromunun neonatal varyantı, intrauterin dönemde başlayan poliürinin neden olduğu ciddi polihidramniyoz ile karakterize otozomal resesif geçişli nadir bir doğumsal renal tübüler bozukluktur. Ağır klinik seyri nedeniyleyaşamı tehdit eden bir durumdur. Burada neonatal Bartter sendromu tanısı konulan iki olgu nadir görülmesi nedeniyle ve uygun sıvı-elektrolit desteğiyle birlikte indometazin tedavisinin erken dönemde başlanmasının doğru bir yaklaşım olacağının vurgulanması amacıyla sunuldu.

Anahtar Kelimeler: Neonatal, Bartter sendromu, renal tübüler bozukluk, preterm doğum, polihidramniyoz, nefrokalsinozis, indometazin

Referanslar

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Telif hakkı ve lisans

Nasıl atıf yapılır

1.
Hakan N, Okumuş N, Aydın M, Zenciroğlu A, Erdoğan Ö, Fettah A, et al. Neonatal Bartter Sendromu: İki Olgunun Sunumu. Turk J Pediatr Dis [Internet]. 2011 Aug. 1 [cited 2025 May 25];5(2):108-13. Available from: https://turkjpediatrdis.org/article/view/141