Abstract

The Pierre-Robin Syndrome (PRS) has been defined in 1902 and consists of three components: cleft palate, mandibular retrognathia and/or micrognathia, and glossoptosis. The mortality rate due to asphyxia is 30% in the syndrome. Another common problem is malnutrition. Intervention may therefore be required to provide a comfortable route for feeding and breathing in the first days of life. Some previously reported approaches are positioning, nasopharyngeal tube usage, intubation and surgical treatment to provide airway patency. However these approaches may be traumatic for the baby and family in the early days of life. In this paper, a 1-day-old PRS case who presented with nutritional and respiratory problems and was later discharged without any problems by the use of an orthodontic palate plaque is presented

Keywords: Feeding difficulties, Orthodontic appliances, Pierre Robin syndrome

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How to cite

1.
Katırcıoğlu M, Güzoğlu N, Aliefendioğlu D. Improvement of Feeding and Respiration with a Palatine Plate in a Case of Pierre-Robin Syndrome. Turk J Pediatr Dis [Internet]. 2017 Dec. 1 [cited 2025 May 24];11(4):280-2. Available from: https://turkjpediatrdis.org/article/view/433