Abstract
Stroke is a significant cause of morbidity in children with sickle cell disease and may recur. The risk of a first stroke is reduced by 90% in patients enrolled in a monthly transfusion exchange program. We report a case of a 9-year-old child who was diagnosed with sickle cell anemia at this delayed age when referred for investigation of the etiology of hemiplegia. The lack of diagnosis and treatment had caused recurrent cerebral infarcts leading to hemiplegia due to multiple vessel occlusions.It is crucial to implement a neonatal screening program for hemoglobinopathies for the early diagnosis of sickle cell anemia. Transcranial Doppler screening should be considered after two years age for patients diagnosed with sickle cell anemia and those with high risk should be enrolled in a monthly transfusion exchange program
Keywords: Child, Hemiplegia, Stroke, Sickle cell anemia
References
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Copyright and license
Copyright © 2016 The Author(s). This is an open access article distributed under the Creative Commons Attribution License (CC BY), which permits unrestricted use, distribution, and reproduction in any medium or format, provided the original work is properly cited.
