Abstract

Anomalous origin of the right pulmonary artery from the ascending aorta (AORPA) is a rare congenital heart defect and generally associated with other cardiac anomalies. Patients with AORPA have high pulmonary fl ow results in congestive heart failure and unilateral pulmonary hypertension. Thus, it is frequently a fatal malformation in the neonatal or early infancy periods if early surgical repair is not performed. Herein, we report a 1.5 month-old girl who was diagnosed with AORPA associated with aortopulmonary window and interrupted aortic arch and successfully operated using a single pericardial xenograft 3D patch

Keywords: Anomalous origin of the right pulmonary artery from ascending aorta, Aortopulmonary window, Congenital heart defect, Interrupted aortic arch

References

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Copyright and license

How to cite

1.
Kocabaş A, Kardelen F, Akçurin G, Mercan Ş, Arslan G, Ertuğ H. Anomalous Origin of the Right Pulmonary Artery from Ascending nomalous Origin of the Right Pulmonary Artery from Ascending Aorta Associated with Aortopulmonary Window and Interrupted orta Associated with Aortopulmonary Window and Interrupted Aortic Arch: Successful Surgical Correction with a Single 3 ortic Arch: Successful Surgical Correction with a Single 3D Patch. Turk J Pediatr Dis [Internet]. 2014 Jun. 1 [cited 2025 May 24];8(3):146-8. Available from: https://turkjpediatrdis.org/article/view/285