Abstract
Henoch-Schönlein purpura is the most common vasculitis of childhood characterized by arthritis/arrthralgia, gastrointestinal and genitourinary system involvement with associated non- thrombocytopenic purpura. Pulmoner involvement is rare, but important because of its higher mortality and morbidity. We present a case of HSP with atypical skin involvement, gastrointestinal and respiratory symptoms. Clinical improvement was achieved after treatment with high-dose methylprednisolone. Because of the high mortality and morbidity in HSP cases with respiratory system involvement, treatment should be fast and intensive.
Keywords: Henöch-Schönlein purpura, pulmoner tutulum
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Copyright and license
Copyright © 2020 The Author(s). This is an open access article distributed under the Creative Commons Attribution License (CC BY), which permits unrestricted use, distribution, and reproduction in any medium or format, provided the original work is properly cited.
