Abstract

Atrial septal defect (ASD) and ventricular septal defect (VSD) are the most common congenital heart anomalies. In this case report, a six-month-old girl with mild pulmonary arterial hypertension (PAH) secondary to ASD and VSD was presented. The patient was admitted due to respiratory failure and renal insufficiency. Evaluation for recurrent extubation failures secondary to left total atelectasis yielded right pulmonary arterial (PA) compression to the left main bronchus. Compression was relieved with right pulmonary arteriopexy with ASD and VSD closure in the same session. The patient was extubated successfully in the immediate postoperative period and eventually discharged home. Bronchial compression should be considered especially in patients with congenital heart disease and recurrent cases of atelectasis in the same location.












Keywords: Atelectasis, Bronchial, Compression

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How to cite

1.
Sincar Ş. A Rare Cause of Bronchial Compression: Mild Pulmonary Hypertension. Turk J Pediatr Dis [Internet]. 2019 Sep. 23 [cited 2025 May 24];13(5):391-4. Available from: https://turkjpediatrdis.org/article/view/581