Introductron:Urticarial vasculitis is a clinicopathological condition characterized by persistent urticarial weals which show vasculitic features on histology. There is evidence that type III hypersensitivity reaction and circulating immune complexes play role in the pathogenesis. The majority of patients are middle aged women. There are limited number of previously reported pediatric cases.

Cases: We herein report four pediatric cases of urticarial vasculitis. The patients were two ( 9 month old and a 2 year old) females and two ( 2 year old and a 10 year old ) males. Urticarial plaques persisted for 4-7 days the patients. The lesions became purpuric and echymotic and healed by leaving hyperpigmentation. Skin biopsy was performed in one patient. In laboratory examination complete blood count, acute phase reactants, serum complement levels, immunoglobulins, ASO titers, AST, ALT levels and urinalyis were performed. Two patients had high sedimentation rate and all four had normal serum complement levels. Other laboratory findings were unremarkable.

Conclusion: Clinical anad laboratory findings of patients have been compared by the literature data. Urticarial vasculitis in pediatric cases and its differential diagnosis have been discusssed

Keywords: Urticaria, vasculitis